The urea cycle (also known as the ornithine cycle) is a cycle of biochemical reactions occurring in many animals that produces urea ((N H 2) 2 C O) from ammonia (NH 3).
The Urea Cycle April 11, 2003 Bryant Miles I. Ammonia Toxicity Every amino acid contains at least one amino group. Therefore every amino acid degradation pathway
Urea cycle defects cause hyperammonemia and may result in coma, convulsions and vomiting during the first few days of life. Clinical confusion with septicemia is ...
A urea cycle disorder or urea cycle defect is a genetic disorder caused by a deficiency of one of the enzymes in the urea cycle which is responsible for removing ...
The urea cycle is smaller than the TCA cycle, and has fewer intermediates. Interestingly, all of the four intermediates are a-amino acids, although three,
The Urea Cycle. Urea is the chief nitrogenous waste of mammals. Most of our nitrogenous waste comes from the breakdown of amino acids. This occurs by deamination.
urea cycle n. The sequence of chemical reactions that takes place in the liver and that results in the production of urea. The key reaction is the hydrolysis of ...
The nitrogen metabolism page provides a discussion of overall nitrogen homeostasis, the production urea for disposal of waste nitrogen, and the clinical consequences ...
A urea cycle disorder is a genetic disorder caused by a mutation that results in a deficiency of one of the six enzymes in the urea cycle. These enzymes are ...
Primary causes of hyperammonemia include congenital enzymopathies in the urea cycle, such as deficiencies of ornithine transcarbamoylase and argininosuccinate lyase.